Incontinentia pigmenti achromians is a rare birth defect that causes unusual patches of light-colored (
Hypomelanosis of Ito (more commonly used)
The cause is unknown. It is twice as common in girls than in boys.
- Hearing problems
- Increased body hair (
hirsutism) Scoliosis Seizures
- Streaked, whirled or mottled patchs of skin on the arms, legs, and middle of the body
- Varying degrees of intellectual disability incluiding autism and learning disability
Exams and tests
A Wood’s lamp examination of the
There is no treatment for the hypopigmentation. Treatment consists of treating the symptoms. Cosmetics or clothing may be used to cover the hypopigmented spots if desired. Seizures, scoliosis, and other problems are treated as necessary.
What happens depends on the type and severity of symptoms that develop. In most cases, the skin pigment eventually returns to normal.
- Discomfort and walking problems due to scoliosis
- Emotional distress related to the physical appearance
- Seizures and resulting possible injury
When to Contact a Medical Professional
Call your health care provider if your child exhibits an unusual pattern of the color of the skin.